Septo-optic dysplasia with olfactory tract hypoplasia
نویسندگان
چکیده
Copyright © Journal of Pediatric Neurosciences Septo-optic dysplasia with olfactory tract hypoplasia Manuel Ribeiro, Álvaro Machado, and João Soares-Fernandes Department of Neuradiology, Hospital de São Marcos, Braga, Portugal. Department of Neurology, Hospital de São Marcos, Braga, Portugal. Address for Correspondence: Dr. Alvaro Machado, Hospital de São Marcos Largo Carlos Amarante Ap 4200 Braga Portugal., Email: [email protected] This is an open-access article distributed under the terms of the Creative Commons Attribution-NoncommercialShare Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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Septo-Optic Dysplasia: A Mini Review
De-Morsier’s syndrome or Septo-optic dysplasia is a rare medical disorder which is strongly associated with CNS, Ophthalmological manifestations. However, in minority of patients, this condition presents with olfactory tract hypoplasia. The CNS abnormalities include abnormalities of the hypothalamicpituitary axis, hypoplasia of the optic nerve. Often, absence of septum pellucidum is seen along ...
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